Case Report


Epithelioid hemangioendothelioma of parapharyngeal space: A rare clinical entity

,  ,  ,  ,  

1 Senior Resident, Department of ENT, AIIMS, Patna, Bihar, India

2 Additional Professor, Department of ENT, AIIMS, Patna, Bihar, India

3 Associate Professor, Department of ENT, AIIMS, Patna, Bihar, India

4 Assistant Professor, Department of Pathology/Lab Medicine, AIIMS, Patna, Bihar, India

5 Senior Resident, Department of Pathology/Lab Medicine, AIIMS, Patna, Bihar, India

Address correspondence to:

Kranti Bhavana

Department of ENT, AIIMS Patna, Phulwarisharif, Patna 801507, Bihar,

India

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Article ID: 100071Z10DK2020

doi: 10.5348/100071Z10DK2020CR

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How to cite this article

Kumar D, Bhavana K, Bharti B, Kumar T, Tiwari P. Epithelioid hemangioendothelioma of parapharyngeal space: A rare clinical entity. J Case Rep Images Oncology 2020;6:100071Z10DK2020.

ABSTRACT


Introduction: An epithelioid hemangioendothelioma is a rare vascular neoplasm primarily of lung, liver, and bones. It is regarded as a neoplasm of borderline or low-grade malignant potential uncommonly seen in head and neck region. It may manifest in other parts of body like breast, lymph nodes, mediastinum, brain, meninges, spine, skin, abdomen, and many other sites. Due to its heterogeneous presentation, rarity, and malignant potential, it is often misdiagnosed and not adequately treated.

Case Report: We herein present a case of hemangioendothelioma of parapharyngeal space in an adult male with progressive swelling in right cervical region. Involvement of parapharyngeal space by this tumor is very rare, which warrants reporting of this case. The dumbbell-shaped tumor was surgically excised in toto and histopathology confirmed the diagnosis.

Conclusion: A wide surgical excision and regular follow-up would be appropriate management. Further research and studies are needed to formulate standardized treatment protocols for this rare tumor.

Keywords: Epithelial hemangioendothelioma, Parapharyngeal neoplasm, Vascular neoplasm

SUPPORTING INFORMATION


Acknowledgments

We express our gratitude to the entire team of Department of ENT and Department of Pathology, AIIMS Patna, India.

Author Contributions

Dheeraj Kumar - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Kranti Bhavana - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Bhartendu Bharti - Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Tarun Kumar - Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Prerna Tiwari - Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Guaranter of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2020 Dheeraj Kumar et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.