Case Series


Desmoid-type fibromatosis of the mesentery with multiple localization presenting as acute abdomen: Two rare case reports in emergency surgery

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1 Department of General Surgery and Specialist Surgeries, Complex Operative Unit of General and Emergency Surgery, Arcispedale Santa Maria Nuova, Azienda Unità Sanitaria Locale - IRCCS di Reggio Emilia, Reggio Emilia, Italy

2 Institute of Advanced Technologies and Experimental Models in Oncology, Complex Operative Unit of Pathological Anatomy, Arcispedale Santa Maria Nuova, Azienda Unità Sanitaria Locale - IRCCS di Reggio Emilia, Reggio Emilia, Italy

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Massimiliano Casadei

General and Emergency Surgery, Arcispedale Santa Maria Nuova, AUSL - IRCCS di Reggio Emilia, Viale Risorgimento 80, 42123 Reggio Emilia,

Italy

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Article ID: 101234Z01MC2021

doi: 10.5348/101234Z01MC2021CS

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How to cite this article

Casadei M, Ricci S, Sergi W, Bollino R, Pucciatti I, Bonilauri S. Desmoid-type fibromatosis of the mesentery with multiple localization presenting as acute abdomen: Two rare case reports in emergency surgery. Int J Case Rep Images 2021;12:101234Z01MC2021.

ABSTRACT


Introduction: Desmoid-type fibromatosis (DF) of the mesentery is a rare entity and the most aggressive form of DF because of its potential to infiltrate abdominal organs and related life-threatening complications.

Case Series: We report two cases of intra-abdominal DF presenting as acute abdomen, which underwent emergency surgical resection, highlighting their presentation, pathologic features, diagnostic workup, and surgical management.

Conclusion: Experienced multi-disciplinary approach is recommended. When active management for DF is necessary, surgery as first-line therapy can be considered, and wide (R0) microscopic margins resection should be the goal.

Keywords: Acute abdomen, Bowel obstruction, Desmoid, Emergency surgery, Fibromatosis, Mesentery

SUPPORTING INFORMATION


Author Contributions

Massimiliano Casadei - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

Stefano Ricci - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

William Sergi - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

Ruggero Bollino - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

Irma Pucciatti - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

Stefano Bonilauri - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published

Guaranter of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2021 Massimiliano Casadei et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.