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Case Report
Fibrous hamartoma of infancy (FHI) of the parotid region in a 3-year-old female presenting as a huge parapharyngeal tumor: A very rare case presentation
1 Senior Resident, Department of ENT, All India Institute of Medical Sciences, Patna, Bihar, India
2 Additional Professor, Department of ENT, All India Institute of Medical Sciences, Patna, Bihar, India
3 Associate Professor, Department of ENT, All India Institute of Medical Sciences, Patna, Bihar, India
4 Professor, Department of Pathology, All India Institute of Medical Sciences, Patna, Bihar, India
Address correspondence to:
Kranti Bhavana
MS, DNB, MAMS, Additional Professor, Department of ENT, All India Institute of Medical Sciences, Phulwari Sharif, Patna 801507, Bihar,
India
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Article ID: 101167Z01RR2020
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Raina R, Bhavana K, Suneha S, Bharti B, Bhadani P. Fibrous hamartoma of infancy (FHI) of the parotid region in a 3-year-old female presenting as a huge parapharyngeal tumor: A very rare case presentation. Int J Case Rep Images 2020;11:101167Z01RR2020.ABSTRACT
Introduction: Fibrous hamartoma of infancy (FHI) is a rare, benign tumor arising from the lower dermis and subcutaneous tissue. It usually occurs in children below two years of age and is often misdiagnosed as being of malignant nature. It most commonly effects the lower extremities, very rarely involves the head and neck region, and is commonly found in males. Microscopically, it is a poorly circumscribed and non-capsulated tumor comprising of interlacing fascicles of pale eosinophilic myofibroblasts and stellate shaped fibroblasts with island of mature adipocytes.
Case Report: We report a very rare case of FHI of parotid gland in a 3-year-old female child, posing a diagnostic difficulty for management. The site, size, and age of presentation of the tumor were unique. This tumor is common in males but our case was a female child. Our patient presented with involvement of the parotid, submandibular and upper neck area with a huge size of around 7 × 8 cm which was causing mild swallowing difficulty due to intraoral swelling in the child. Cytopathology from the lesion demonstrated spindle cell lesion, the differential diagnosis of which is often malignant in pediatric age group. We took a biopsy for confirmatory diagnosis and after histopathological diagnosis of FHI proceeded with complete surgical excision.
Conclusion: Treatment of choice for these benign tumors is complete surgical excision, with excellent prognosis.
Keywords: Fibrous hamartoma of infancy, Myofibroblasts, Parapharyngeal tumor, Parotid
SUPPORTING INFORMATION
Author Contributions
Ragini Raina - Substantial contributions to conception and design, Acquisition of data, Analysis of data, Interpretation of data, Final approval of the version to be published
Kranti Bhavana - Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Swati Suneha - Substantial contributions to conception and design, Drafting the article, Final approval of the version to be published
Bhartendu Bharti - Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Punam Bhadani - Acquisition of data, Analysis of data, Interpretation of data, Drafting the article, Final approval of the version to be published
Guaranter of SubmissionThe corresponding author is the guarantor of submission.
Source of SupportNone
Consent StatementWritten informed consent was obtained from the patient for publication of this article.
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2020 Ragini Raina et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.
